Behra SK, Choudhary A, Mishra D, Behera B, Dei K

Rosai Dorfman disease, originally described as sinus histiocytosis with massive lymphadenopathy is a rare disorder in India. This disease is unique for its bilateral massive lymph node enlargement in the neck, associated with high erythrocyte sedimentation rate, leukocytosis and fever. Although cervical region is by far the most common and prominent site, it can affect other peripheral and central lymph node groups, skin and gastro-intestinal tract. We report this rare disease diagnosed by fine needle aspiration cytology and subsequently confirmed by histopathological examination.

Key words : sinus histiocytosis with massive lymphadenopathy, lymph node, cytology